Primary hemangioblastoma of the left kidney and epithelioid leiomyoma of the right

Hemangioblastoma is a rare benign tumor; common by found in the central nervous system, about 25% is associated with Von Hippel-Lindau (VHL) disease. Renal hemangioblastoma is extremely rare. The leiomyoma generally occurs in organs with abundant of smooth muscle such as uterus, gastrointestinal tract or subcutaneous soft tissue. It’s unusual to see it in the kidney, while the renal epithelioid leiomyoma is even more unusual. Here, we describe a rare case of renal hemangioblastoma and epithelioid leiomyoma occurring in a 43-year-old female without clinical evidence of VHL disease.